Desarrollo neuromuscular en la atrofia muscular espinal 

    Martínez Hernàndez, Rebeca (Date of defense: 2012-11-23)

    BACKGROUND: Spinal muscular atrophy (SMA) is a neuromuscular disease characterized by degeneration and loss of spinal cord motor neurons leading to denervation and muscular atrophy. It is caused by defects in the Survival ...